Biliary Atresia

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Long case presentation

(Biliary Atresia)

Dr. Sajal Debnath


Phase-A resident
Dept. of paediatric surgery
MMCH
Particulars of the patient
• Name : Asif
• Age : 2.5 months
• Sex : Male
• Religion : Islam
• Address : Gouripur, Mymensingh
• Date of admission : 20/09/23
• Date of examination : 05/10/23
Chief complaints
• Yellow discoloration of eyes and skin since
birth.
• Persistent pale colored stool and dark colored
urine since 07 days of age.
History of present illness
• According to the statement of the patient’s
mother,he was born with yellow discoloration
of both eye and skin which was progressive in
nature. Mother also noticed persistent pale
colored stool and dark colored urine since 7
days of his life. Mother gave no history of poor
feeding, vomiting,fever, itching and bleeding
manifestation.
History of past illness
• The patient was admitted in paediatric dept.
of MMCH 01 month back with the same
complaints and treated conservatively. They
are also advised some ivestigations on
discharge but she couldn’t show any paper.
Birth history
• Antenatal history : She was not in regular ANC.
• Natal history : he was delivered by normal
vaginal delivery, birth weight 2.4kg.
• Post natal history : uneventful.
• Feeding history : exclusive breast feeding
• Developmental history : age appropriate
• Immunization history : only BCG vaccine was
given.
• Family history : the baby was the 3rd issue of
the non consanguineous parents, parents are
in good health, no family history of liver
disease or same type of illness.
• Socioeconomic history: His socioeconomic
history is average.
General examinations
• Appearance : ill-looking.
• Pallor : mildly pale
• Jaundice : moderately icteric
• Dehydration : absent
• Edema : absent
• Cyanosis : absent
• Clubbing : absent
• Koilonychia: absent.
• Leuconychia : absent
• Lymph node : not palpable
• Anterior fontanel : open, normal
• Skin survey : BCG mark present.
Vital signs
• Temp : 98°F
• Pulse : 90b/min
• Res. Rate : 24b/min
• Length : 55cm
• OFC : 35cm
GIT
• Mouth and oral cavity : yellowish
discoloration.
• Abdomen :
• Inspection : shape is scaphoid in shape, flanks
are not full,umbilicus centrally placed &
inverted,no engorged vein,visible peristslsis or
any scar mark. Hernial orifices are intact.
• Palpation : abdomen is soft, non tender.
Liver: liver is palpated, 5 cm from right costal
margin and in mid-clavicular line, non-tender, firm in
consistency, surface is smooth, margin is Sharp, upper
border of liver dullness is at rt 4th intercostal space.
Spleen: not palpable.
• Percussion : tympanic, shifting dullness absent.
• Auscultation : bowel sound present.

Other systemic examination reveals no


abnormality.
Salient feature
• Asif, a 2.5 months old male baby, 3rd issue of
his non-consanguineous parents hailing from
gouripur, mymensingh, got admitted with the
complaints of progressive jaundice, passage of
persistent pale stool and dark colored urine
since 4th day of life. there was no history of
poor feeding, vomiting, fever, itching and
bleeding manifestation.
• He was admitted in paediatric dept. Of MMCH
01 month back with the same complaints and
treated conservatively. They are also advised
some investigation on discharge but she
couldn’t show any paper. He was born NVD at
term.
• On general examination – he was ill looking,
mildly pale, moderately icteric.
• On systemic examination – mouth and oral
cavity shows yellowish discoloration.
• On palpation- liver is palpated 5 cm from right
costal margin and in mid clavicular line. Liver is
non-tender, firm in consistency, surface is
• Smooth, margin is Sharp, upper border of liver
dullness is at 4th intercostal space.

• Other system examination reveals normal.


Provisional diagnosis
• Obstructive jaundice may be due to biliary
atresia.
Differential diagnosis
• Neonatal hepatitis.
• Choledochal cyst.
Investigations
• CBC with blood grouping
• Liver function test
• USG of HBS
• HIDA scan
Treatment

• The Roux-en-Y hepatic Portoenterostomy


procedure.(Kasai procedure).
• Liver transplantation.

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