PEDS Exam 2 - Outline
PEDS Exam 2 - Outline
PEDS Exam 2 - Outline
Disorder
Differences in Anatomy and Physiology of the Neurologic System of Children
o First 3 to 4 weeks’ gestation
Infection, trauma, teratogens, and malnutrition can cause physical defects and may
affect normal CNS development.
o Birth
Cranial bones well developed, but not fused: increased risk for fracture.
Brain is highly vascular: increased risk for hemorrhage.
o Child
Spinal cord is mobile: high risk for cervical spine injury.
o If something is wrong with neuro, it will be detrimental to growth and development
o Preemies are at risk for brain problems
o Myelination is going to occur which helps gross motor and fine motor skills
Proportions of Head to Body Height in Newborn, Child and Adult
o
o In a baby, the head is a quarter of the body while in an adult it is 1/8 of the body
o Assessment of the growth trend of the head is important in detecting potential neurological
conditions
Types of Neurologic Disorders in Children
o Structural disorders
o Seizure disorders
o Infectious disorders
o Trauma to the neurologic system
o Blood flow disruption disorders
o Chronic disorders
o It is important to check LOC first followed by vital signs
Common Types of Structural Defects
o Neural tube defects
Majority of the congenital anomalies of the CNS
Folic acid supplementation can decrease the incidence of NTDs
o Anencephaly
Defect in brain development resulting in small or brain hemispheres, skull and scalp
o Microcephaly
Smaller than normal head circumference
May be congenital or acquired and develop in the first few years of life
Caused by abnormal development during gestation or follow intrauterine infections
such as rubella, toxoplasmosis and cytomegalovirus
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o Arnold–Chiari malformation
Usually associated with hydrocephalus and myelomeningocele resulting from the
cerebellum, medulla oblongata and fourth ventricle displacing into the cervical canal
resulting in an obstruction of the CSF and causing hydrocephalus
o Hydrocephalus
Larger than normal head circumference
Results when there is an obstruction in the ventricular system and the venous
channels
o Intracranial arteriovenous malformation
Caused by an abnormal development of blood vessels and can occur in brain,
brainstem or spinal cord
o Craniosynostosis
Premature closure of the cranial sutures which can inhibit brain growth and a
distorted skull appearance will be evident
Hydroencephalus and increased ICP are more likely to appear
o Extra Notes
Some patients with hydrocephalus can look normal, while others will have the
typical large head
Children with shunt are more likely to have developmental problems
Spongy fontanel sign of increased ICP
Depressed fontanel is a sign of dehydration
Intracranial AVM can occur anywhere in the brain, brainstem or spinal cord and if it
hemorrhages, it can lead to neuro problems or death
Past Medical History Findings Related to Neurologic Disease in Children
o Prematurity
o Difficult birth: ask mom to tell you about the birth.
o Infection during pregnancy
o Falls
o Recent trauma
Common Signs and Symptoms Related to Neurologic Disease in Children
o Nausea, vomiting: is an early indicator of incr. ICP
Brain tumor sign: vomiting early in the morning. Then the pt is not able to walk
o Headaches (early morning, frequent, or persistent)
o Changes in gait
o Loss of motor function
o Visual disturbances: seeing flutters
o Changes in level of consciousness (LOC) or confusion: earliest indicators
o Increased irritability lethargy: late signs
o Altered muscle tone: meningitis or lethargy
Measure head circumference until age 3
o LOC earliest indicator of improvement or degradation
o NEED TO KNOW PEDIATRIC GCS
5 Different LOC states (pg 476)
o Full consciousness – defined as a state in which the child is awake and alert, is oriented to
time place and person and exhibits age-appropriate behaviors
o Confusion – defined as a state in which disorientation exists. The child may be alert but
responds inappropriately to questions
Ex: kids may ask where there mom is, but mom is there.
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o Obtunded – defined as a state in which the child has limited responses to the environment
and falls asleep unless stimulation is provided
o Stupor – exists when the child only responds to vigorous stimulation
Painful stimulation
o Coma – defines a state in which the child cannot be aroused even with painful stimuli
Prenatal Risk Factors for Neurologic Disorders
o Prematurity
o Maternal drug or alcohol use during pregnancy
Common for baby to have a drug withdrawal
Start w/ morphine then get weaned off to methadone
o Maternal infection during pregnancy
o Maternal ingestion of teratogens
o Fetal malnutrition in utero
Risk Factors for Birth Trauma
o Multiple deliveries
o Large-for-date infants
o Infants with extreme prematurity
o Infants with a large fetal head: maybe from fetal alcohol symptoms
o Infants with congenital anomalies
Common Laboratory and Diagnostic Tests
o Lumbar puncture (LP)#1 go to!, CSF analysis
Withdrawal of CSF from the subarachnoid space for analysis
o Intracranial pressure (ICP) measurements
Sensing device place in the head used to monitor ICP resulting from
hydroencephalus, acute head trauma, and brain tumors
Ventricular catheter allows for draining of CSF to reduce ICP
o Electroencephalogram (EEG)
Measures electrical activity of the brain to diagnose brain seizures and brain death
o Head and neck radiograph
Radiographic image of the head and neck to detect skull and spinal fractures
o Ultrasound
o Fluoroscopy
X-ray of vertebral blood vessels to assess for vessel defects or space-occupying
lesions
o Computed tomography (CT), magnetic resonance imaging (MRI), positron emission
tomography (PET), and single photon emission computed tomography (SPECT)
Other Procedures and Treatments for Neurologic Disorders
o Ventricular shunt placement
Catheter is placed in the ventricle to pass the CSF to the peritoneal cavity, atrium of
the heart, or pleural spaces
Commonly used in hydrocephalus or increase ICP
Rovisions:
o Hyperventilation
Used to decrease PaCO2 which will result in vasoconstriction and therefore decrease
ICP
o Physical, Occupational, or Speech Therapies (PT/OT/ST)
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Therapies are used to improve motor function and ability of children with neurologic
disorders
Used for head injury, or intellectual disability
o External ventricular drainage (EVD)
A catheter is temporarily placed in the ventricle and CSF is drained in a closed
system to an external reservoir
Commonly used with shunt infections until CSF is sterile and shunt can be replaced
EVD direct access to spinal cord and so child with be in ICU
o Ventricular tap
Go into the shunt To reduce accumulation of CSF and decrease ICP
o Vagal nerve stimulator
A nerve stimulator is implanted and a lead wire running under the skin is wrapped
around the vagus nerve and is programmed to stimulate at certain intervals
Used for short and long term seizure management in children older than 12 years old
o Ketogenic diet
Diet involving a high intake of fats, adequate protein and very low intake of carbs
Used for prevention, control and reduction of seizures
Inspection and Observation of a Child With a Neurologic Disorder
o Level of consciousness (LOC)
o Vital signs
Baby check the reflexes
Do neuro test
Sunsetting: eyes point downwards. Seen in a pt w/ a shunt
Review decerebrate (hands and feet turn out) and decorticate ( coming into the core)
o Head, face, and neck
o Cranial nerve function
o Motor function
o Reflexes
o Sensory function
o Increased intracranial pressure (ICP)
o Chart 16.1
Medications Used to Treat Neurologic Disorders
o Antibiotics
Treatment of bacterial meningitis and shunt infections
Kill and prevent growth of bacteria
o Anticonvulsants
Decrease hyperexcitability of nerves
Treatment and prevention of seizures
o Benzodiazepines
Minor sedative that prevents or stops seizures by slowing down the CNS, making
abnormal electrical activity unlikely
Ex: xanax
o Analgesics
Block pain impulse in response to inhibition of prostaglandin synthesis
Narcotic analgesics act on receptors in the brain to alter perception of pain. Used to
treat pain. Used to help avoid increase in ICP
Propohyl and ketamine: it helps with pain. Fast acting, acts for about 10 min.
children have shaking eyes.
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o Osmotic diuretics
Increase plasma osmolality, therefore inducing diffusion back into plasma and
extravascular space/reduces ICP
o Corticosteroids
Suppress inflammation and normal immune response/reduce cerebral edema
Common Types of Seizures
o Febrile seizure: does not need an intervention unless it lasts longer than 5 minutes.
Check temperature and blood sugar.
o Kids w/ seizures longer than 5 min get diastat (diazepam- anxiolytic, sedative).
o Parents need to change medications when child going to growth spurt. Stress and not
going enough sleep can increase the risk of seizures.
o Need to know where they were, what were doing before the seizure, what did it look like
and how long did it last, and what happened before and after.
o Infantile spasms:
o Absence
Brief interruption in consciousness without loss of postural control
Staring off into space
May have hand gestures, blinking and chewing
o Tonic-clonic
Begins with LOC change, stiffening and then jerking. They will have that time frame
where the mind is not there.
o Myoclonic
Single jerk of one or more muscles, lasting seconds
Consciousness usually is preserved
o Atonic
Sudden loss of muscle tone (drop attack)
o Simple partial
Seizure that occurs in one part of the brain
o Complex partial
May begin with a focal seizure without impaired consciousness and then progress
o Status epilepticus
Febrile seizures are the most common type seen in children less than 5 years
Commonly occurs early in the course of epilepsy and can be life threatening
o Extra Notes
If child just had a seizure, then pain will be done via FLACC scale
Status epilepticus is an emergency as it happens for longer than 5 mins
Diazepam used in febrile seizures going on for more than 5 mins
Febrile seizures depend more on how quickly their fever goes up instead of how high
the fever can go
Febrile seizures usually do not have permanent brain damage
Febrile seizures are usually related to a viral illness
Seizures have to be within 24 hours apart to be considered a seizure
Seizure meds cannot be abruptly stopped and must be weaned off
Weaning off doesn’t occur unless seizure free for at least two years
Have suction and oxygen at the bedside, padding of the hand rails.
Ativan is the go to drug. They can also be on phenobartibal are the drug they are on
at home. They have to have their labs checked continually and be compliant
Types of Infectious Disorders of the Neurologic System
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o Bacterial meningitis
Infection of the meninges, the lining that surrounds the brain and spinal cord
Can occur as secondary infection of upper respiratory infections, sinus infections or
ear infections or direct introduction through LP, skull fracture or severe head injury
Hib vaccine has reduced incidences of this
Sensitive to light, neck pain, and vomiting are big signs
o Aseptic meningitis (viral)
Most common type of meningitis and majority of children infected are less than 5
years
Causative organism is usually a virus especially enteroviruses
o Encephalitis
Inflammation of the brain that may also include an inflammation of the meninges
Caused by protozoan, bacterial, fungal or viral invasion
Swelling of the bain
o Reye syndrome (rare)
Affects children less than 15 years
Reaction triggered by the use of salicylates or salicylate-containing products to treat
a viral infection
o Extra Notes:
Bacterial meningitis usually seen after sepsis
Child can deteriorate in 24 hours with meningitis and gold standard for testing is
lumbar puncture
If known for sure that it is viral, then antibiotics will not be given
Reye syndrome caused by aspirin
Encephalitis is inflammation of brain caused by virus, bacteria or fungal can come
from herpes or vector born. Can cause brain damage if not treated quickly. Can even
by caused by chemo.
Intracranial Pressure (ICP)
o CNS has a dynamic balance of fluid (called CSF) that bathes the brain and spinal cord at a
specific pressure called intracranial pressure (ICP).
o Elevated ICP is a sign of a neurologic disorder.
o Possible causes: head trauma, birth trauma, hydrocephalus, infection, brain tumors.
o Try and limit pain such as preventing crying because it will increase ICP
o Child will have a shrill cry which is common and parents will know the difference
Early Versus Late Signs of Increased Intracranial Pressure
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o Know this chart!
o Vomiting and headache are big ones especially with babies since they can’t say that they
aren’t feeling well
o Shunt patients have heart rate all over the place and will be on pulse ox to monitor pulse
o Main late sign is bradycardia and posturing
o Brain damage w/ repeated concussions
o Shunt malformation or infection will need to be on a pulse O2 and it can get really low.
o Seizures from bulging fontanelle
Hydrocephalus
o Caused by an imbalance in the production and absorption of CSF.
o May see signs of ICP including increase in head size and loss of developmental milestones or
changes in personality in older children.
o May require surgical intervention to relieve pressure with a ventricular shunt (temporary or
permanent).
o Prepare parents for surgery, babies will have a shrill cry due to increase in irritability from
malformation or infection.
Parents know to look for sunset eyes.
o Sometimes it is seen in utero. Can have surgery before the baby is born
Signs and Symptoms of Shunt Infection
o Elevated vital signs
o Poor feeding
o Vomiting
o Decreased responsiveness
o Seizure activity
o Signs of local inflammation along the shunt tract/ see infection on the shunt
o Kids will grow so the shunt will need multiple revisions
Common Causes of Head Trauma in Children
o Falls
o Motor vehicle accidents
o Sports injuries
o Pedestrian and bicycle accidents
o Child abuse: shaking baby syndrome. Coup to coup injury.
Causes of Nonaccidental Head Trauma
o Violent shaking: shaken baby syndrome (SBS)
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o Blows to the head
o Intentional cranial impacts against the wall, furniture, or the floor
o Seen if there is no prenatal care, younger parents who get aggravated from baby
o Extra Notes:
SBS occurs because of knocking against the skull back and forth
Concussion in kids under a year gets CT scan but if over a year, they will have
questions asked as well such as if they were vomiting or have been eating or drinking
before they get a CT
After concussion they will be on brain rest so no studying or playing games etc.
If head injury, adult has to be with child every 24 hours and wake them up every few
hours to observe them and make sure everything is okay
Parent has to wake up every 2 hours to check on the child w/ a concussion.
If they haven’t vomited just check on the child.
If there is an injury, stabilize the neck.
Common Head Injuries Seen in Children (Table 16.6)
o Skull fractures – a break in the bone surrounding the brain
o Linear skull fracture – a simple break in the skull that follows relatively straight line
o Depressed skull fractures – the bone is locally broken and pushed inward, causing pressure on
the brain
o Diastatic skull fracture – a fracture through the skull sutures
o Compound skull fracture – a laceration of the skin and splintering of the bone
o Basilar skull fracture – a fracture of the bones that form the base of the skull
o Concussion – a type of traumatic brain injury that is caused by a bump, blow, jolt, jarring, or
shaking and results in disruption or malfunction of the electrical activities of the brain
o Contusion – bruising of cerebral tissue
o Subdural hematoma – collection of blood between the dura and cerebrum
o Epidural hematoma – collection of blood located outside the dura but within the skull
Acute Stroke in Children
o Ischemic or hemorrhagic types.
o Risk factors in children are different than in adults.
o Will see same signs and symptoms as in adults.
Weakness on one side or hemiplegia
Facial droop
Slurred speech
Speech deficits
o Usually rare in kids except for sickle cell anemia children
Blood transfusions helps child w/ stroke
Managing Disturbed Sensory Perception
o Assess for changes in sensory perception.
o Monitor child for risk of injury secondary to changes in sensory perception.
o Notify physician or nurse practitioner of changes in sensory perception.
o Assist child to learn to use adaptive methods to live with permanent changes in sensory
perception (i.e., use of eyeglasses) and maximize the use of intact senses.
o Provide familiar sounds (voices, music).
Pediatric Glasgow Coma Scale
o Objective measure of child’s LOC by assigning numerical values to the presence of
developmentally appropriate clues (eye-opening, verbal response, and motor response).
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o Memorize this for the exam
o
Closed Head Injuries
o Brain injury graded on severity (mild, moderate, severe) based on symptoms.
o May occur with an accident or intentional injury.
o Nonpenetrating injury to head.
o Normal behavior before the injury, may or may not lose consciousness.
o Skull fx does not get any interventions, but just watching them while in the hospital. Watch
out for bleeding to see changes in LOC
Promoting Child and Family Teaching
o Assess child’s and family’s willingness to learn.
o Provide family with time to adjust to diagnosis.
o Repeat information.
o Teach in short sessions.
o Gear teaching to a level of understanding of the child and family.
o Provide reinforcement and rewards.
o Use multiple modes of learning involving many senses.
o Near drownings can cause a lot of injuries such as long-term neuro effects
Defined as an incident in which a child has suffered a submersion injury and has
survived for at least 24 hours
Near drownings in children younger than 1 years old can occur in bathtubs, toilets or
buckets
Children between 1 – 4 years are more likely to drown in residential swimming pools
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For children older than 15, drowning occurs in oceans or lakes
Classifications of Pain
Duration
o Acute: tissue damage(sore throat, appendicitis) or chronic- not protective (cancer)
o Kids in chronic pain cannot grow or meet milestones as fast as normal.
Etiology
o Nociceptive: stimulus that damages the tissue (stabbing, chemical burns) or neuropathic:
peripheral or CNS(tingling, spasms) Vincristine: tx for leukemia, but causes neuropathic pain.
Kids will walk on their tippy toes. Vincristine also causes constipation
Source/location
o Somatic: superficial (organs-sharp stab pain, paper cut) or visceral: deep pain(kidney failure,
ulcerative colitis, skin-arm cut, nausea, vomiting diaphoresis, )
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Exposure to pain at an early age has little or no effect later.
Infants and small children have little memory of pain.
Intensity of the child’s reaction to pain indicates intensity of pain.
A child who is sleeping or playing is not in pain.
Children are truthful when asked if they are in pain.
Children learn to adapt to pain and painful procedures.
Children are more prone to addiction to narcotic analgesics.
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Word-graphic rating scale (ages 8 to 15, child selects pain rating)
Visual analog and numeric scales (ages 3+, scales of 0–10)
Adolescent pediatric pain tool (ages 8 to 15, measures pain location, intensity and quality)
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Routes for Pain Medication Administration
Preferred routes:
o Oral, rectal, intravenous, topical, or local nerve block routes
o Epidural administration and conscious sedation also can be used.
o PCA pumps are for sickle cell patients
Respiratory system:
o respiratory rates DECREASE; respirations are diaphragmatic in nature
o age 7 lungs mature
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Cardiovascular system:
o Blood pressure INCREASE and pulse rate DECREASES.
o Heart decreases in size
Immune system:
o matures to adult level around 10 years old; fewer infections experienced
Gastrointestinal system:
o Deciduous teeth replaced by permanent teeth; fewer gastrointestinal upsets; stomach capacity
increases; caloric needs are lower but appetite may increase.
Genitourinary system:
o Bladder capacity increases (age in years + 2 ounces) ex: age 9. 9+2=11 ; prepubescence occurs 2
years before puberty. Breast buds and growing of the testicles .
Musculoskeletal system:
o Greater coordination and strength; muscle still immature and can easily be injured.
Caloric needs are lessened.
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Peer relationships-most important relationships to them
Teacher and school influences
Family influences
Make sure they know the plan and stick to the plan.
Erickson: figuring out what they can achieve or what they can do. They are developing self worth, and. Build
on things. Give them easy things and then build up on it. start collecting things-Barbie’s, Pokémon cards.
Paiget: concrete operational learns by manipulating objects, no abstract thinking, understands time. They
can finally see perceptions that are not their won. Start collecting things. Start to understand conservation
such as water turning into ice, steam, etc.
Kohlberg: follow the golden rules, follow religion. They want to be. Good person
Freud: same sex friends. All girls or all boys. Relate to the opposite gender parent. Mom and son, dad and
daughter
Safety Issues:
Car safety-do not sit in front, out of booster=over 12years or over 80lbs.
Pedestrian safety
Bicycle and sport safety
Fire safety
Water safety-swim lessons: at age 5
Abuse in children
Assessing Nutrition:
Check height and weight compared to previous measurements; assess BMI for age.
o 95% is obese, 85-95%: overweight
Nutrition history including a 24-hour recall of what was consumed.
Inquire about family meals and the social aspects of eating including who prepares the meals.
Solicit from both parent and child.
Identify any knowledge gaps relating to nutrition.
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Whole grain breads and cereals
Non-fat (skim) or low-fat milk
Developmental Concerns:
Television and video games (setting limits on both the
content and amount of time)
School refusal (school phobia)
Latchkey children and safety-kid gets left home alone
Stealing, lying, cheating, bullying (whether as the perpetrator or the victim) teach prevention
Fitting in with peer groups
Tobacco and alcohol education
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Medical care (including transportation to care)
Mental health and education services
Physical, occupational, or speech therapy
Treatment for emotional, developmental, or behavioral problems
Financial assistance
Family support
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Focus of Nursing Management of Children With Special Needs
Case management and advocacy
Screening and ongoing assessment of the child
Provision of appropriate home care
Care of the technology-dependent child
Education and support of the child and family
Referral for resources
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Individual with Disabilities Education Act (2004) requires local school systems to provide for the education
of children with special needs through the public school system, from age 3 to 21 years.
Education is usually provided in the local school system.
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Focus of Palliative Care
Managing pain and discomfort
Providing nutrition
Providing emotional support to the dying child and family
Assisting the family through the grief process
Chapter 20: Nursing Care of the Child with an Alteration in Bowel Elimination/Gastrointestinal Disorder
Percussion
o Tympanic sound? Dull?
Palpation
o Supine if possible, warm hands, avoid tickling, place hand on top
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If the child is in diapers, use a tongue blade to scrape a specimen into the collection container.
If the child has runny stool, a piece of plastic wrap in the diaper may catch the stool specimen. Very liquid
stool may require application of a urine bag to the anal area to collect the stool.
The older ambulatory child may first urinate in the toilet, and then the stool specimen may be retrieved
from the new or clean collection container that fits under the seat at the back of the toilet.
For the bedridden child, collect the stool specimen from a clean bedpan (do not allow urine to contaminate
the stool specimen).
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o May occur separately or in combination
o Leakage of the esophagus
Clinical Presentation
o Polyhydramnios while in utero
Inability to handle secretions, cyanosis while feeding
o Resistance when passing a feeding tube
o drooling
o 5 types-don’t need to know
Diagnostics
o Xrays show coiling, Ultrasound of Renal System, Echo, of contrast evaluation
Nursing Interventions
o Surgery NPO, fluids, TPN, elevate the head to prevent aspiration, help them not cry. **
o Prevention of aspiration
o Tube in proximal pouch
o Iv antibiotics and fluids prior to surgery in supine postion
o Chest Tube Care, elevated HOB 30 to 45 degrees, frequent suctioning with premeasured catheter,
tube feedings 2 to 3 days after surgery, if no leak, start oral feedings 5 to 7 days after *remove
Chest tube then*
o Make sure to keep in chest tube unless the child is actually able to eat
o
o FIGURE 20.7 Esophageal atresia and tracheoesophageal fistula. A. The most common type of
esophageal atresia, in which the esophagus ends in a blind pouch and a fistula connects the trachea
with the distal portion of the esophagus. B. The upper and distal portions of the esophagus end in a
blind pouch. C. The esophagus is one segment, but a portion of it is narrowed. D. The upper
portion of the esophagus connects to the trachea via a fistula.
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Anomalies and Complications Associated With Cleft Lip and Palate
Seen in 1 in 700 children
Seen in utero about 2-3 months
Fix lip around 2-3 months
Fix palate when they hit a certain weight
Want to get these surgeries done before 12 months b/c they need to learn how eat again
Anomalies
o Heart defects
o Ear malformations
o Skeletal deformities
o Genitourinary abnormality
Complications
o Feeding difficulties encourage breastfeeding
o Altered dentition
o Delayed or altered speech development
o Otitis media- not eating correctly-not draining properly
• Affects ears.
o Protect the suture line!!!!
o Post op- mittens on hands to avoid baby touching the stiches
• No suction/sucking no pacifier and straws, sippy cups
• Avoid crying & provide emotional support
• May supine or sidelying
• NPO immediately after surgery
• Keep the child calm
• Breastfeeding can still be done
• Haverman feeder- still allows them to suck b/c they are at risk for aspiration
• Check respiratory and nutrition.
Celiac disease
Also known as gluten-induced enteropathy or celiac sprue
Permanent GI intolerance to dietary wheat and related proteins
o Four characteristics
• Steatorrhea
• General malnutrition
• Abdominal distention
• Secondary vitamin deficiencies
See 15-3
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o Endoscopy and tissue biopsy for definitive diagnosis
Nursing Interventions and Education
o Teach patients and family about gluten free diet
o Encourage Support Groups
o Treat dehydration if necessary
o Avoid Wheat, barley, and Rye
Acute GI Disorders
Dehydration, vomiting, and diarrhea
Oral candidiasis and oral lesions
Hypertrophic pyloric stenosis
Necrotizing enterocolitis
Intussusception, malrotation, and volvulus
Appendicitis
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o Most diarrhea is spread by the fecal-oral route, make sure the water supply is clean and
protected from contamination, prepare food carefully, wash hands
Nursing Management of the Newborn with Omphalocele (born without a sac outside of the body) or
Gastroschisis (born with a sac outside of the body)
Goals
o Preventing hypothermia, maintaining perfusion to the eviscerated abdominal contents by
minimizing fluid loss, and protecting the exposed abdominal contents from trauma and infection.
Intervention
o Cover the abdominal contents with a non-adherent sterile dressing avoiding trauma to the
intestine, cover with plastic wrap to minimize heat and fluid loss; prevent abdominal distention
with low suction to orogastric tube, monitor fluid status.
Chronic GI Disorders
Gastroesophageal reflux, peptic ulcer disease
Constipation/encopresis
Hirschsprung disease
Short bowel syndrome- on bolus feedings (avoid TPN because you cannot live on TPN and may cause
liver issues/transplant)
Inflammatory bowel disease
Celiac disease
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Recurrent abdominal pain
Failure to thrive and chronic feeding problems
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Monitor H&H and get a CBC
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Chapter 21: Nursing Care of the Child with an Alteration in Elimination/Genitourinary Disorder
UTI’s continued
Contributing factor is urologic instrumentation
o Allows bacteria present in the opening of the urethra to enter the urethra or bladder
Sexual intercourse promotes “milking” of bacteria from the perineum and vagina
o May cause minor urethral trauma
o Diagnostics
Urinalysis is affordable, will show leukocyte, possible RBC’s, casts, but nitrites are the
gold standard
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Upper tract infection involves the renal parenchyma, pelvis, and ureters
Typically causes fever, chills, and flank pain
Lower tract infection involves the lower urinary tract
Usually no systemic manifestations
A urine culture must be obtained after urinalysis in order to confirm the right antibiotics
o Parents should be encouraged to follow up for a repeat urine test
o Avoid bubble bath, rubber panties, wipe from front to back,
Antibiotics for treatment (follow up to make sure the antibiotic is relevant to the cultures)
Urinalysis
Normal Urinalysis
o pH: 5.0 to 8.5
o Specific gravity: 1.001 to 1.035
o Protein: Less than 20 mg/dl
o Urobilinogen: Up to 1 mg/dl
o None of the following:
Glucose
Ketones
Hemoglobin (Hgb)
White blood cells (WBCs)
o NITRATES ARE THE GOLD STANDARD FOR UTI!!!!!!!!
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o UTI
o Enuresis
o Nephrotic syndrome
o Acute glomerulonephritis
o Hemolytic-uremic syndrome
o Renal failure (acute and chronic)
Nephrotic syndrome:
o Most common presentation of glomerular injury in children
o Characteristics:
Massive proteinuria
Hypoalbuminemia
Hyperlipidemia
Edema
o Minimal change disease (most common) constitutes 80% of cases
Also known as Idiopathic nephrosis
Childhood nephrosis
Minimal lesion nephrosis
o Assessment
Often occurs after an URI (upper resp. infection), peaks in children between 2 and 5
Edema is gravity dependent and occurs gradually and occurs around the eyes,
scrotal/sacral, asicities (wake up swollen-throughout the day the swells spreads) first in
the face-by the end of the day-ankles
Weight gain, decreased UOP, anorexia (not hungry but still gaining weight), easily
fatigued, and HTN increase in blood pressure
PROTEINURIA & EDEMA
o Treatment
o Supportive Care-teach parents how to do a dip stick and perform daily weights
o Diet
Low to moderate protein
Sodium restrictions when large amounts of edema are present
o Steroids (first line of therapy)
Dose is 2 mg/kg divided into twice-a-day doses
Prednisone is the drug of choice (least expensive and safest)
At risk for infection (lowers the immune respsonse)
At a very high risk of infection. (this is a priority)
Runny nose, sore not healing
o Diuretics
LASIX
o IV albumin infusion (pull of the extra fluid)
o Strict monitoring of daily weight
o Immunosuppressant's in non-responsive to steroids
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o Facial edema is more prominent in the morning
o Spreads during the day to involve the lower extremities and abdomen
o Coca-cola urine due to kidney spilling out protein and RBCs
Hypertension due to increased extracellular fluid
Oliguria (severely reduced volume)
Hematuria
o Bleeding in the upper urinary tract, results in “tea or Coca-Cola urine”
Proteinuria
o Increased amount of protein signifies increased severity of renal disease
Renal Failure
Condition in which the kidneys cannot concentrate urine, conserve electrolytes, or excrete waste products.
May be acute or chronic
o When acute renal failure continues to progress, it becomes chronic (also known as end-stage renal
disease [ESRD]).
Dialysis and kidney transplantation are treatment modalities used for ESRD.
o Peritoneal dialysis is preferred
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Persistent scratching of the irritated area may result in the complication of superficial
skin infection.
Pelvic inflammatory disease
o Manifestations of Pelvic Inflammatory Disease (PID)
Fever
Abdominal pain
Pain with intercourse
Dysmenorrhea (painful menstrual cycles)
Abnormal uterine bleeding
Long-term complications
Chronic pelvic pain, ectopic pregnancy, and infertility related to scarring.
Sexually transmitted infections
Menstrual disorders
o Primary and secondary amenorrhea (over exercising, anorexia)
o Mittelschmerz and dysmenorrhea
o Menorrhagia and metrorrhaghia
Genitourinary Anomalies
Cryptorchidism
o Undescended testis
Correction between 6 and 18 months
Hypospadias
o Congenital anomaly of the male urethra
Incidence 1/250-300 live births
Genetic and environmental factors
Abnormal ventral placement of the urethral opening of the underside of the penis,
ranging from the glans to the perineum
o Severity- based on position of the urethral opening and the chordee (ventral curvature of the penis)
Surgery between 6 and 12 months
Goals of Surgery
o Enhance the child’s ability to void in the standing position with a straight stream
o Improve the physical appearance of the genitalia for psychological reasons
o Make sure sperm is coming out of the proper area that they wont be infertile
o Preserve a sexually adequate organ
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Benefits and Complications of Circumcision
Benefits
o Decreased incidence of UTI, sexually transmitted infections, AIDS, and penile cancer, and in
female partners a decreased occurrence of cervical cancer.
o Gauze stays on for 24hrs
o Keep area moist with Vaseline
Complications
o Alterations in the urinary meatus, unintentional removal of excessive amounts of foreskin, or
damage to the glans penis. BLEEDING
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Urinary diversion Vesicostomy
Foley catheter Appendicovesicostomy
Ureteral stent Bladder augmentation
Nephrostomy tube Dialysis (hemodialysis and peritoneal)
Suprapubic tube
Nursing Goals for the Child With End Stage Renal Disease (ESRD)
Promoting growth and development.
Removing waste products and maintaining fluid balance via dialysis.- peritoneal dialysis is preferred as a
child.
o Assess the child receiving peritoneal dialysis for toleration of the fluid volume instilled within the
peritoneum.
Minimize complications by maintaining adequate fluid and nutrition. (RISK OF UTI’S)
Can be born with non-functioning kidneys.
Encouraging psychosocial well-being.
Supporting and educating the family.
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Primary enuresis: enuresis in the child who has never achieved voluntary bladder control.
Secondary enuresis: urinary incontinence in the child who previously demonstrated bladder control over a
period of at least 3 to 6 consecutive months.
Diurnal enuresis: daytime loss of urinary control.
Nocturnal enuresis: night time bedwetting.
Rule out medical- do urinalysis first
Boys longer to potty train- up to 5-6 y/o, due to being in a deep sleep and won’t wake up to pee.
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Organ System Maturation (Adolescent) #2
Musculoskeletal system: linear growth is not complete until late adolescence in boys and occurs earlier in
girls; growth plates (which promote linear growth) begin to close at puberty. Adult height is attained when
growth plates have closed in late adolescence
Integumentary system: skin is thick and tough; sebaceous glands are more active; sweat glands function at
adult level
Developmental Theories–Adolescence
Piaget: indent movement, they believe what they believe: black lives matter,
Kohlberg: they look at the world. Internal to themselves. They believe what they believe. They tend to think outside
of the present
Ways to Improve Communication with Teens
Allow sufficient time for conversation
Speak respectfully as you would to a colleague
Talk face to face; be aware of body language (yours and the teen’s)
Ask open-ended questions to clarify and promote understanding
Reflect back what you think you heard so that he or she feels heard
Choose words carefully so that message and intent are clear
Be honest; don’t be afraid to say you don’t know
Be liberal with praise; acknowledge effort
Solicit the teen’s input in decision making as often as possible
Clearly state expectations and set limits fairly
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Serve as credible sources of information and social reinforcement (behaviors, roles)
Can have positive or negative influences
Provide education to the teen regarding nutritional value of favorite foods and suggest better alternatives
for those with lower nutritional value
Provide resources for online and community resources about nutrition (MyPyramid.gov)
Emphasize the role of physical activity in maintaining healthy weight; provide healthy physical activity
options not related to sports (60 minutes per day is recommended)
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Appropriate discipline
Mental health resources
Common Substances Abused by Children and Adolescents (page 202-KNOW slang terms)
Marijuana (including synthetic marijuana) Dextromethorphan (cough syrup)
Alcohol Bath salts
Prescription opiates, sedatives, and Hallucinogens
analgesics Inhalants (inhaling fumes from aerosol
Prescription stimulants (Adderall, Concerta, household products)
Ritalin) Cocaine, crack
Prescription CNS depressants (barbituates, Heroin
benzothiazides, sleeping aids)
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QUESTIONS:
Is the following statement true or false? The most common reason for admission to the hospital for children with
congenital heart disease is heart failure.
True. The most common reason for admission to the hospital for children with congenital heart disease is
heart failure.
Rationale: Heart failure occurs most often in children with CHD and is the most common reason for
admission to the hospital for children with CHD. Heart failure also occurs secondary to other conditions
such as myocardial dysfunction prior to or following surgical intervention for CHD, cardiomyopathy,
myocarditis, fluid volume overload, hypertension, anemia, or sepsis, or as a toxic effect of certain
chemotherapeutic agents used in the treatment of cancer.
The nurse is assessing a child for cardiac disorders and documents the presence of clubbing of the fingers and toes.
Which of the following conditions might this indicate?
a. Infection b. Cyanosis
c. Edema d. Hypoxia
Rationale: The sign of an infection is fever. Cyanosis is a bluish tint to the skin due to decreased oxygenation.
Edema is swelling or bloating due to fluid imbalance.
1. The nurse accurately explains to a child’s parents that the point at which a person feels the highest intensity of a
painful stimulus is termed the pain threshold. False. The point at which a person feels the lowest intensity of a
painful stimulus is termed the pain threshold.
Rationale: In addition to sending a message to the cerebral cortex, the thalamus also sends a message to the
limbic system, where the sensation is interpreted emotionally, and to the brain stem centers, where autonomic
nervous system responses begin.
2.The nurse assessing pain in children is correct in stating that the school-age child is usually able to communicate
the type, location, and severity of pain. True. The school-age child is usually able to communicate the type,
location, and severity of pain.
3.The nurse is assessing the pain of a 3-year-old child. Which of the following pain assessment scales would be most
appropriate?
a. Visual analog scale b. Visual numeric scale
c. Word-graphic rating scale d. FACES pain rating scale
Rationale: The FACES pain rating scale is a self-report tool that can be used by children as young as 3 or 4 years of
age. The word-graphic rating scale is useful for children between 4 and 17 years old. The visual analog scale can be
used with children 7 years or older. The numeric scale can be used with children 8 years or older.
5.The school nurse conducting a vision screening program identifies a child with amblyopia. Both eyes were noted
to have visual acuity less than expected for the child’s age.
False. Amblyopia, or lazy eye, occurs when one eye is more nearsighted, farsighted, or astigmatic than the other eye
causing an imbalance in vision.--> Rationale: Malalignment of both eyes is referred to as strabismus.
6.The nurse obtains a nutrition history for a school-age child. The parent indicates the child’s favorite beverage is
apple juice and consumes three large glasses per day. The mother asks if this is a good thing. Which of the following
would be the best response for the nurse to reply to the mother?
A. Apple juice is very healthy. Keep up the good work!
b. Apple juice has quite a bit of sugar and no fiber. Could you substitute an apple for one of those servings?
c. As long as your child drinks plenty of fluids, she will be fine.
b. An 8-ounce serving of apple juice has about 24 g of sugar—the equivalent of 3 teaspoons of sugar, with
none of the fruit fiber that would be available in a whole apple. Rationale: Children need both fruit and fiber daily
as part of a healthy diet. Apple juice, while made from apples, concentrates the sugar and takes out the fiber. Water
and milk are good alternatives for beverages.
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7.The nurse is caring for a school-age child with cerebral palsy. Which of the following developmental tasks,
appropriate for this age, may be delayed?
a. Attachment to family
b. Sense of independence
c. Achieving industry
d. Forming a sense of identity
8.The Individuals with Disabilities Education Improvement Act (IDEA) of 2004 mandates federal government-
funded care coordination and special education for children up to 12 years of age.
False. The Individuals with Disabilities Education Improvement Act (IDEA) of 2004 (formerly called Public Law
99-457) mandates local government-funded care coordination and special education for children up to 21 years of
age.
9.The nurse initiates transition planning for adulthood when the patient reaches 21.
False. Transition planning is complex and requires education for the parent and child and coordination of services
long before the age of majority (18 years of age in most states).
10.The nurse is caring for a child with diarrhea related to infectious enteritis. The nurse accurately informs the
parents that most cases of diarrhea are bacterial in nature and therapeutic management is usually supportive in
nature.
False. Most cases of diarrhea are viral in nature and therapeutic management is usually supportive in nature
11.The nurse is auscultating the bowel sounds of a 4-year-old child and documents hypoactive bowel sounds. What
might this finding indicate?
a. Obstruction. Hypoactive bowel sounds indicate obstruction. b. Gastroenteritis
c. Diarrhea d. Infection
12.The nurse is assessing the cognitive development of an adolescent. Which of the following statements accurately
represents a normal finding at this stage?
a. the adolescent progresses from an abstract to a concrete framework of thinking
b. the adolescent develops the ability to think outside the present
c. all adolescents achieve formal operational reasoning at the same time
d. adolescent thinking starts out very introspective and then becomes egocentric
13.The nurse caring for an adolescent should educate the parents about the importance of monitoring their
adolescent’s interaction with peer groups.
True. The nurse caring for an adolescent should educate the parents about the importance of monitoring their
adolescent’s interaction with peer groups.
14.Suicide is the third leading cause of death in adolescents 15 to 19 years of age. True. Suicide is the third leading
cause of death in adolescents 15 to 19 years of age.
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Cardiovascular Changes in Childhood
Heart Rate.
o Faster in infancy (~120–130 bpm), decreases as the child ages.
o Nothing above 160.
Blood Pressure.
o Lower in infancy (~80–55 mmHg), increases as the child ages.
Respiratory Rate.
o Faster in infancy, decreases as the child ages.
By adolescence, values approach adult levels.
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Pulse oximetry: most commonly used
Electrocardiogram (ECG) and Holter monitoring.
Cardiopulmonary monitoring: cardiac monitoring and Pulse Oximetry
Echocardiogram
Chest radiograph
Exercise stress testing
Laboratory tests including: CBC, BMP, C-reactive protein (CRP) (inflammation) , Erythrocyte
sedimentation rate (ESR)
Arteriogram and cardiac catheterization
Congenital Heart Disease with Increased Pulmonary Blood Flow- PDA (NCLEX)
Patent ductus arteriosus- Should close within 72 hours of birth normally.
o May be indicated by
Heart Murmur-systolic murmur, mid to lower-left sternal border, Washing machine
sound (LEFT TO RIGHT SHUNTING)
Wet sounding breath sounds, crackles
Tachypnea, Increased WOB, or Apnea
Poor Feeding, poor weight gain and growth pattern, fatigue, sweating with feeding,
excessive fluid weight gain b/c heart is pumping harder
o Diagnosis
Wide pulse pressure- low diastolic pressures and high systolic
Poor oxygen sats
Bounding Pulses, Prolonged cap refill
Enlarged Heart, Echo shows enlarged left heart chamber
o Nursing Interventions
Decrease WOB (work of breathing) by providing rest periods, no clustered care, strict
I&O, DIGOXIN, give indomethacin or ibuprofen(keep it open until it can be surgically
repaired), monitor labs for thrombocytopenia, daily weights, provide prep for surgical
closure, and teach parents to watch fluid intake
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o Should close normally at 4-8 weeks in fetal development up to 1 year, but this will cause more
blood flow into the right side of the heart, increasing pulmonary blood flow
Assessment
o Heart murmur, know as ejection systolic murmur due to blood forced from pulmonary valve, can
have atrial dysrhythmias and increased risk for emboli/ clot
o Recurrent URI’s, but few symptoms in children
o Can have SOB, tires easily while playing, poor feeding & poor growth if CHF develops (extra
fluid)
o Liver enlargement
DX
o Echo show enlargement of right atrium and right ventricle
o EKG show thickening of the heart muscle
o Chest X-ray shows enlarged heart and increased blood flow to lungs
Medical Management and Nursing Interventions
o Give digoxin and diuretics to decrease the load on the right side of the heart
o Provide pain medications to decrease O2 consumption
o Cardiac Cath to patch the hole
o Offer small frequent meals and feedings
o Monitor for s/s of CHF
o Monitor for increased WOB, grunting, retractions and flaring
o Caregiver Education- Look for bleeding (apply pressure if there is bleeding at the cardiac cath
site), antibiotics for dental work, follow up
Risk for endocarditis
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o Chest X-ray-Left heart cardiomegaly
Nursing Interventions
o Same as ASD
Surgical Interventions
o Will suture or patch the hole
o Occurs during first 6 to 12 months of life when the infant is over 2000 g so that when they patch
the site they don’t have to go back in.
Not as bad due to the location
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o Teach parents the “Tet” hold (make smallpush legs up to chest to increase blood flow to the
heart/oxygen to the brain so that hypoxia is decreased)
o Requires multiple surgeries.
o Child may squat (tet Squad) to get more oxygen.
Tricuspid Atresia
Defective or missing Tricuspid Valve, decreased blood flow to lungs
Assessment
o Cyanosis, SOB
o Delayed Growth and poor weight gain
o Murmur due to ASD that is normally present
o Clubbing of fingers in older kids
DX
o Echo, EKG, Chest X-ray, Cardiac Cath
Nursing
o Prepare child for surgery, and multiple surgeries, requires immediate surgery for survival
o Nurse must maintain prostaglandin E1 administration
o Requires immediate surgery, but will require ECMO
o Use digoxin
Education
o Life-long cardiology care with multiple surgeries
o Monitor for fluid retention, fast heart rate, and chronic diarrhea
o Monitor for SOB, bluish color, or slow growth
Eisenmenger Syndrome
“Hole in the heart”, damage to the heart
Must be fixed right away.
ECHMO
No baths after surgery
No vigorous play, don’t get then upset, cluster care
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o Can be caused from group A Strep
Causes CP, fatigue, exercise intolerance causing death, monitor for s/s of CHF, decrease
in cardiac output
Pulmonary stenosis-extra work on the heart-lead to pulm edema and heart failure
Pulmonary atresia
Tetralogy of fallot with pulmonary atresia
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Congestive heart failure (C H F)
o Impaired myocardial function
Tachycardia, fatigue, weakness, restlessness, pale, cool extremities, decreased blood
pressure, decreased urinary output
o Pulmonary congestion
Tachypnea, dyspnea, respiratory distress, exercise intolerance, cyanosis
o Systemic venous congestion
Peripheral and periorbital edema, weight gain, ascites, hepatomegaly, neck vein
distention
o Nursing Interventions
Monitor VS frequently; report s/s increasing distress, Assess respiratory function
frequently
Elevate HOB or use infant seat, Oxygen as prescribed
Administer digoxin and diuretics as prescribed
Daily weights, Strict I/O, Report unusual weight gains
Low-sodium diets or formula, breast feeding is recommended. Gavage (NGT) feedings if
NPO due to distress, Cluster care
Often associated with acyanotic defects
Condition in which the heart is unable to pump effectively the volume of blood that is
presented to it.
Common complication of CHD.
Reflects the increased workload of the heart caused by shunts or obstructions.
Goals for treatment: 1) reduce the workload of the heart 2) increase cardiac output
Before administering digoxin, nurse must take child’s apical pulse x 1 minute to assess for bradycardia.
Hold dose if pulse is below normal heart rate (below 90-100) for child’s age.
Therapeutic blood levels of digoxin are 0.8- 2.0 ng/mL.
Keep in a safe place (i.e. locked cabinet)
Families should be taught safe home administration of digoxin:
• Administer on a regular basis; do not skip or make up for missed doses
• Give 1 hour before or 2 hours after meals Do not mix with formula or food
• Take the child’s pulse before admin, and know when to call the caregiver
Nurse must be acutely aware of the signs of digoxin toxicity. A small child or infant cannot describe
feeling bad or nauseated.
o Vomiting is a common EARLY sign of toxicity. This symptom is often overlooked because
infants commonly “spit up.”
o Teach parents about compliance. They must know the difference btwn the chil
o LATE SIGN: bradycardia
o Other GI symptoms include anorexia, diarrhea, and abdominal pain.
o Neurological signs include fatigue, muscle weakness, and drowsiness
o Hypokalemia can increase digoxin toxicity
Improves contractility
Increased cardiac output
Decreased heart size
Decreased venous pressure
Relief of edema
In children, digoxin (Lanoxin) is used almost exclusively because of its more rapid onset.
Note the dose is calculated in micrograms (1000 mcg = 1 mg).
During initiation, the child is monitored by means of an ECG to observe for the desired effects (prolonged
PR interval and reduced ventricular rate) and detect side effects, especially dysrhythmias.
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Infective Endocarditis
Bacterial infection of endothelial surfaces of the heart including valves (most common), chamber walls, or
septum.
Children with prosthetic valves are at higher risk than general population.
Diagnosed based upon modified Jones Criteria
o Modified Jones Criteria (American Heart Association) (Table below)
Acute rheumatic fever diagnosis requires presence of 2 major criteria or 1 major +
2 minor criteria
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Watched the rest of their life. Ask “have you had a sore throat” (strep throat)
ESR and CRP are elevated due to inflammation
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Aching bones
Pain in joint: arthralgia
Cardiomyopathy
Definition: inflammation of the myocardium so that it cannot contract properly.
Types: restrictive, dilated and hypertrophic.
Risk factors include:
o Congenital heart defect, genetic disorders, inflammatory or infectious processes, post-transplant or
postoperatively after cardiac surgery, hypertension, Duchenne and Becker muscular dystrophy.
Most commonly, no known reason (idiopathic).
May present as heart failure or cardiac arrest (in adolescents with hypertrophic version).
Treatment: targets improving heart function.
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Past Health History
Problems occurring after birth (associated congenital malformation).
Birth history (any NICU stays?)
Frequent infections.
Chromosomal abnormalities.
Prematurity.
Autoimmune disorders.
Use of medications, such as corticosteroids.
Additional Disorders
Hyperlipidemia, Hypertension
Rheumatic heart disease (scarlet fever)
o Inflammatory disease occurring after group A beta-hemolytic streptococcal pharyngitis (GABHS)
Infrequently seen in the United States; big problem in developing countries
o Self-limiting
Affects joints, skin, brain, serous surfaces, and heart
o Most common complication of RF
Damage to valves as a result of RF (rheumatic Fever)
Jones criteria (presence of two major manifestations or one major manifestation and two minor
manifestations)
o Carditis, Polyarthritis, Erythema marginatum, Subcutaneous nodules, Chorea
o Erythema marginatum: similar to the Lyme disease rash
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o Subcutaneous Nodules: are deep-seated lesions in the skin, located in the deep dermis and
subcutis,
Subacute bacterial endocarditis
o Bacterial endocarditis (BE) and subacute bacterial endocarditis (SBE) are now referred to as
infective endocarditis (IE)
o Often a sequela of bacteremia in children with CHD or AHD
o Most common causative agents
Streptococcus viridans or Staphylococcus aureus
Fungal agents such as Candida albicans
Psychosocial Interventions
Explain all that is happening with the child, using language the parents and child can understand.
Allow the parents and child to voice their feelings, concerns, or questions.
Provide ample time to address questions and concerns.
Encourage the parents and the child, as developmentally appropriate, to participate in the child’s care.
Encourage the child to be as active as is appropriate.
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Postprocedural Care
o Check the pulse distal to the site
o Monitor the temperature and color of extremities
o Take the vital signs every 15 minutes
o Monitor the blood pressure
o Monitor the dressing for bleeding or hematoma
o Monitor intake and output
o Monitor blood glucose levels
Chapter 24: Nursing Care of the Child With an Alteration in Cellular Regulation/ Hematologic or Neoplastic
Disorder
Types of Anemia
Nutritional deficiency
o Iron deficiency(switch from cow’s milk to formula, and during puberty), folic acid deficiency,
pernicious anemia(lack of b12)
Toxin exposure
o Lead poisoning
Aplastic anemia
o Acquired as an adverse reaction to medication
o Rare congenital bone marrow failure (Fanconi anemia)
Hemolytic anemia
o Sickle cell anemia, thalassemias, hemophilia
Hematologic Disorders
Iron-deficiency anemia
o Caused by an inadequate supply of dietary iron
o Generally preventable
o Predictable at developmental periods
In premature infants, due to low fetal supply
At 12 to 36 months, due to ingestion of large amounts of cow’s milk and diet
In adolescents, due to rapid growth and poor eating habits
o Most common type of anemia
Not enough healthy R B C's
Diminished oxygen-carrying capacity of blood
Screen at 12 months
To treat
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Transfusion if needed, below 7 and symptomatic
Nutritional supplement (Vit. D)
Types of Hemoglobinopathies
Sickle cell anemia
Hemoglobin SC disease
o α-Thalassemia
o β-Thalassemia
Hematologic Disorders
Sickle cell disease
o Ethnicity
AUTOSOMAL RECESSIVE both parents have to have the gene makeup
Occurs primarily in African Americans
Occurs in 1 in 375 infants born in the United States
One in 12 has sickle cell trait
o Occasionally also in persons of Mediterranean descent
o Also seen in persons of South American, Arabian, and East Indian descent
o If both parents have the trait, each child of theirs will have a 1 in 4 likelihood of having the disease
o Partial or complete replacement of normal hemoglobin with abnormal hemoglobin S (Hgb S)
Hemoglobin in the RBCs takes on an elongated “sickle” shape
Sickled cells are rigid and obstruct capillary blood flow
Microscopic obstructions lead to engorgement and tissue ischemia
Hypoxia occurs and causes sickling, leading to pain
Usually pain happens in the same part of the body
o Large tissue infarctions occur
Damaged tissues in organs; impaired function
o Splenic sequestration
Ask if they still have their spleen
May require splenectomy at an early age
Results in immunity
o Don’t want sickle in the brain b/c it can cause stroke
o Meds keep the cells from being sticky and the other stops the blood from clotting
o Only cure is a bone marrow transplant
o Acute chest syndrome if sickle cell affects the lungs
o Heart attack if sickle cell affects the heart
o Dactylitis: swelling of fingers and toes. Affected by sickle cell
o Sickle cell in the spleen: the spleen will be removed
o Priapism: sickle In the penis and they have elongated erection
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Stasis of blood with clumping of cells in the microcirculation leads to ischemia
and then infarction
Signs are fever, pain, and tissue engorgement
Aplastic Crisis
Diminished production and increased destruction of RBCs
Triggered by viral infection or depletion of folic acid
Signs include profound anemia and pallor
• Nursing Management
Monitor the child’s growth and watch for failure to thrive
o Carefully do a multisystem assessment
Assess and treat pain
Observe for the presence of inflammation or possible infection
Carefully monitor for signs of shock
Promote growth and development
Goals
o Prevent sickling phenomena
o Treat medical emergencies
Childhood vaccines
Aggressive treatment of infection
Possible prophylactic antibiotics in children from 2 months to 5 years of age
ONLY bone marrow treatment to cure SS anemia
Make sure to give lots of fluids
Babies w/ sickle cell will be on penicillin until age 5
Hydroxyurea: helps restore fetal blood supply.
Hemophilia
A group of hereditary bleeding disorders that result from deficiencies of specific clotting factors
Typically, an X-linked recessive pattern
Hemophilia A
o Classic hemophilia (deficiency of factor VIII (8))
o Accounts for 80% of cases of hemophilia
o Kids will bring in their own factor medication (expensive for the hospital)
o At risk for nose bleeds, bleeding after procedures
o If they bleed a lot use Rest, ice, Compression and also give them Factor 8
o Give them desmopressin for mild hemophilia.
Hemophilia B
o Christmas disease (deficiency of factor IX (9))
Von Willebrand disease (vWD)
o Deficiency, abnormality, or absence of vWF and factor VIII
o Affects both males and females
Hemarthrosis
o Bleeding into joint spaces of the knee, ankle, or elbow leads to impaired mobility and,
eventually, bony changes and disability
o Symptoms include warmth, pain, bruising, and decreased movement
At risk for epistaxis, bleeding after procedures, and GI Bleeding
Avoid sports
Medical Management of Hemophilia
o Replacement of missing clotting factors
o Desmopressin (DDAVP)
IV
Increases factor VIII activity by two to four times
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Used for mild hemophilia
o Transfusions
Prompt intervention to reduce complications
o Medications
o Exercise and physical therapy joints
Make sure bones are moving
Nursing Care Management
• Prevent bleeding episodes
• Recognize and control bleeding
• Support the patient
o Pain
o Mobility
o Promote growth and development
• Support the family
o Education
o Prepare for home care
• Interventions
o Close supervision and safe environment
o Dental procedures in a controlled situation
o Shave only with an electric razor
o For superficial bleeding, apply pressure for at least 15 minutes and ice to promote vasoconstriction
• If significant bleeding occurs, transfusion for factor replacement
Managing Hemarthrosis:
During bleeding episodes, elevate and immobilize the joint
Ice
Analgesics
Range-of-motion exercises after the bleeding stops will help to prevent contractures
Physical therapy
Avoid obesity to minimize joint stress
The nurse is caring for a child with anemia caused by a deficiency in vitamin B12. What type of anemia is this child
experiencing?
a. Pernicious anemia
Rationale: Thalassemia and sickle cell anemia are a result of hemolytic disorders and folic acid deficiency is caused
by low dietary intake of green leafy vegetables, liver, citrus, or malabsorption of medication.
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o Thalassemia intermedia: child requires blood transfusions to maintain adequate quality of life.
o Thalassemia major: to survive, the child requires ongoing medical attention, blood transfusions,
and iron removal.
o Treatment: blood transfusion-will reach a phase where the body won’t accept/fix with the blood
support family
o Ask their baseline hemoglobin
Clotting Disorders
• Idiopathic thrombocytopenia purpura (ITP)
o Body attacking itself and
• Henoch–Schönlein purpura
• Disseminated intravascular coagulation (DIC) (can’t clot)
o Happens usually during sepsis
o factors 2,5,8,10
o Septic shock,
• Factor deficiencies
o Hemophilia A (factor VIII deficiency)
o von Willebrand disease
o Hemophilia B (Christmas disease, factor IX deficiency)
o Hemophilia C (factor XI deficiency)
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o rhabdomyosarcoma (multiple sites)
o retinoblastoma
60
• Abnormal liver function tests with elevated bilirubin.
Sources of Lead
• Paint in homes built before 1978 and dust from windowsills, walls, and plaster in older homes.
• Soil from sites where cars that used leaded gas had been parked.
• Glazed pottery and stained glass products.
• Lead pipes supplying water to the home.
• On the clothing of parents who work in certain manufacturing jobs.
• Certain folk remedies, such as greta or arzacon.
• Old painted toys or furniture .
Chapter 26: Nursing Care of the Child With an Alteration in Metabolism/ Endocrine Disorder
Endocrine System
Hormones are turned out during puberty
Composed of glands, tissues, or clusters of cells that produce and release hormones in a negative feedback
system involving the hypothalamus and nervous system.
Influences all physiologic processes
o Growth and development.
o Metabolic processes related to fluid and electrolyte balance and energy production.
o Sexual maturation and reproduction.
o The body’s response to stress.
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o Maintenance of internal homeostasis.
Cortisol levels are high during stress
Adrenal glands.
Question #1
The nurse is caring for a child diagnosed with juvenile diabetes. Which of the following medical treatments
would be appropriate for this child?
d. Glucose monitoring
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Complications of Growth Hormone Deficiency and Therapy
Altered carbohydrate, protein, and fat Slipped capital femoral epiphysis (SCFE)
metabolism Pseudotumor cerebri
Hypoglycemia Leukemia
Glucose intolerance/diabetes Recurrence of CNS tumors
o They stay in the hospital for 3 days Infection at the injection site
to educate family members Edema and sodium retention
Pituitary Disorders
Anterior hormones
o Growth hormone deficiency
o Hyperpituitarism
o Precocious puberty
Posterior hormones
o Diabetes insipidus
o Syndrome of inappropriate antidiuretic hormone secretion
Hyperpituitarism
Growth hormone excess
Acromegaly
Marfan’s syndrome
Syndrome of inappropriate antidiuretic hormone (S I A D H)
o Produced by hypersecretion of the posterior pituitary (increased ADH)
Signs and symptoms include fluid retention and hypotonicity
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Kidneys are unable to reabsorb water
Anorexia, nausea and vomiting, irritability, and personality changes
Symptoms disappear when ADH is decreased
o Nursing Management
Accurate I&O, diet high in protein and sodium, medications with meals
Observe for signs of fluid overload
Seizure precautions, Neuro checks
Administer ADH-antagonizing medicines
Fluid Restriction is key
Precocious Puberty
Defined as sexual development before age 9 years in boys; before age 7 years in Caucasian girls; or before
6 years in African-American girls
o Occurs more frequently in girls
Three types
o Central precocious puberty (CPP) (80%)
o Peripheral precocious puberty (PPP)
o Incomplete precocious puberty (IPP)
Treatment of specific cause if known
Central variety is treated with leuprolide acetate (Lupron Depot)
o Slows prepubertal growth to normal rates
o Treatment is discontinued at the age at which normal pubertal changes would resume
Psychological support for the child and family
Question #2: The nurse is caring for a child with diabetes insipidus. Which of the following clinical manifestations
would be expected for this child?
b. Serum osmolality greater than 300 mOsm/kg
Rationale: Other clinical manifestations of diabetes insipidus include urine specific gravity less than 1.005,
decreased urine osmolality, hypernatremia, increased urination, and dehydration/thirst.
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o Mostly seen as Graves Disease.
o Exophalmos: big eyes
o Very hyperactive
o Excessive T3, T4, T3 resin uptake.
o TSH usually low.
o Eyes bulged, nervousness, heat intolerance
o Treated by destruction of thyroid gland.
o Will be on Synthroid
o Must have compliant parents.
Hypothyroidism: can be congenital or acquired diagnosed much later.
o Certain populations at risk (Downs, maternal hypothyroidism).
o Decreased thyroid hormones.
o Tiredness, constipation, cold intolerance
o Thin hair, gained weight
o Decreased T3, T4, T3 resin uptake.
o TSH usually elevated.
o Lifelong thyroid supplementation.
Classification of Diabetes
Type 1: caused by a deficiency of insulin secretion due to pancreatic β-cell damage.
Type 2: consequence of insulin resistance that occurs at the level of skeletal muscle, liver, and adipose
tissue with different degrees of β-cell impairment.
Diabetes secondary to certain conditions such as cystic fibrosis, glucocorticoid use (as in Cushing
syndrome), and certain genetic syndromes such as Down syndrome, Klinefelter syndrome, and Turner
syndrome .
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Signs and Symptoms of Diabetic Ketoacidosis
Anorexia, nausea and vomiting. they need insulin. They will use Short acting
Lethargy, stupor, altered level of insulin which is Regular (Humulin or
consciousness, confusion. Novolin)
Decreased skin turgor.
Abdominal pain.
Kussmaul respirations and air hunger. In the mean time , while waiting for insulin
Fruity (sweet-smelling) or acetone breath drip given them bolus IV NS. Push fluids
odor. until the insulin is obtained
Presence of ketones in urine and blood.
o Check urine and see for ketones
Tachycardia, and if left untreated, coma and
death. Kids need to be put on a pump. When they
have diabetes . cant be on a pump if pt is
When kids are admitted with DKA they noncompliant. Teach and educate parents.
need an insulin drip. When they are sick
Give pt a snack before and after exercising.
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Promoting positive adjustment to the disease, with ability to self-manage in the home.
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